Classification of Kidney Diseases

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@Glomerular Diseases

I. Primary Glomerular Diseases
Minimal change nephrotic syndrome (MCNS)

Focal segmental glomerulosclerosis (FSGS)

Membranous glomerulonephritis (nephropathy)

Mesangial proliferative glomerulonephritis

IgA nephropathy (nephritis),

Henoch-Schonlein purpura nephritis

Non-IgA nephritis

Membranoproliferative glomerulonephritits (MPGN)

Crescentic glomerulonephritis

Goodpasture syndrome

II. Glomerulonephritis of Systemic Diseases

Lupus nephritis

IgA nephropathy (nephritis) and Henoch-Schonlein purpura nephritis

Glomerular lesions in systemic infections

Poststreptococcal glomerulonephritis (PSGN)

Human immunodifficiency virus-associated nephropathy (HIVAN)

Hepatitis B/C virus-associated nephropathy

III. Glomerular Lesions in Vascular Diseases

Nephrosclerosis (benign and malignant)

Anti-neutrophil cytoplasmic autoantibody (ANCA)-associated nephritis

Thrombotic microangiopathy (Hemolytic uremic syndrom)

IV. Hereditary Nephropathies

Diabetic nephropathy

Amyloidosis

Dense-deposit disease

Immunoglobulin deposition diseases

V. Miscellaneous Glomerular Diseases

* Terminology

Diffuse (>80%) and focal (<80%)

Global and segmental

Glomerulonephritis, glomerulonephropathy

Nephritis and nephropathy

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